Specific codes in ICD-10 are unique alphanumeric designations used to identify and categorize diseases, disorders, and conditions. They consist of 3-5 characters, including both letters and numbers, that provide a high level of detail and specificity.
| Language | Translation |
|---|---|
English
|
Neuronal ceroid lipofuscinosis |
French
|
Lipofuscinose à céroïdes neuronaux |
| Level | Code | Title | |
|---|---|---|---|
| 1 | IV | Endocrine, nutritional and metabolic diseases | |
| 2 | E70-E90 | Metabolic disorders | |
| 3 | E75 | Disorders of sphingolipid metabolism and other lipid storage disorders | |
| 4 | E75.4 | Neuronal ceroid lipofuscinosis |
| Active Ingredient | Description | |
|---|---|---|
| Cerliponase alfa |
Cerliponase alfa is a recombinant form of human tripeptidyl peptidase-1 (rhTPP1). Cerliponase alfa is a proteolytic inactive proenzyme (zymogen) that is activated in the lysosome. The glycosylation profile of cerliponase alfa results in consistent cellular uptake and lysosomal targeting for activation. |
