ICD-10 Specific code E76.1: Mucopolysaccharidosis, type II

Specific codes in ICD-10 are unique alphanumeric designations used to identify and categorize diseases, disorders, and conditions. They consist of 3-5 characters, including both letters and numbers, that provide a high level of detail and specificity.

Translations

Language Translation
Flag for English language  English Mucopolysaccharidosis, type II
Flag for French language  French Mucopolysaccharidose, type II

Hierarchical position

Level Code Title
1 IV Endocrine, nutritional and metabolic diseases
2 E70-E90 Metabolic disorders
3 E76 Disorders of glycosaminoglycan metabolism
4 E76.1 Mucopolysaccharidosis, type II

Indicated medicines

Active Ingredient Description
Idursulfase

Idursulfase (idursulfase) is a purified form of the lysosomal enzyme iduronate-2-sulfatase, produced in a human cell line providing a human glycosylation profile, which is analogous to the naturally occurring enzyme. Elaprase is indicated for the long-term treatment of patients with Hunter syndrome (Mucopolysaccharidosis II, MPS II).