Active Ingredient: Chenodeoxycholic acid
Chenodeoxycholic acid is indicated for the treatment of inborn errors of primary bile acid synthesis due to sterol 27-hydroxylase deficiency (presenting as cerebrotendinous xanthomatosis (CTX)) in infants, children and adolescents aged 1 month to 18 years and adults.
For this indication, competent medicine agencies globally authorize below treatments:
Oral
5 - 5 mg per kg of body weight
From 1.667 To 1.667 mg per kg of body weight 3 time(s) per day every day
The starting dose in children is 5 mg/kg/day in three divided doses. Where the dose calculated is not a multiple of 250 mg, the nearest dose below the maximum of 15 mg/kg/day should be selected, provided that is sufficient to normalise serum cholestanol and/or urine bile alcohols.
It can be taken without regards to food.
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